Pulmonary atresia, intact ventricular septum, and Ebstein anomaly of the tricuspid valve
نویسندگان
چکیده
منابع مشابه
Pulmonary Valve Atresia with Intact Ventricular Septum.
A case of pulmonary valve atresia with intact ventricular septum' with long survival in the absence of a patent ductus arteriosus, is presented. The patient, alive at 21 years of age, has the anterior descending branch of the left coronary artery originating from the pulmonary artery. Thus, the pulmonary blood supply is obtained from the right coronary artery via intercoronary anastomoses. No s...
متن کاملCongenital absence of the pulmonary valve associated with tricuspid atresia and intact ventricular septum.
visualized. The left circumflex coronary artery showed an area of 50 percent narrowing prior to its bifurcation into the obtuse marginal branch. In addition, there was a significant 70-80 percent stenosis at the origin of the obtuse marginal branch, with no distal circumflex coronary artery visualized. The right coronary artery was a large vessel and was totally occluded at the acute margin, wi...
متن کاملThe electrocardiogram in tricuspid atresia and pulmonary atresia with intact ventricular septum.
MOST PATIENTS with cyanotic congenital heart disease show right axis deviation and right ventricular hypertrophy of more or lesser degree in the electrocardiogram. Left axis deviation by contrast has long been recognized as the cornerstone of the diagnosis of tricuspid atresia.1 Although occasionally the A QRS is between 0° and +90° or may deviate slightly to the right in this condition, anatom...
متن کاملPulmonary atresia with intact ventricular septum
OBJECTIVES We describe the morphologic variability in pulmonary atresia with intact ventricular septum (PAIVS) within a population-based study. BACKGROUND An uncommon disease, PAIVS shows considerable morphologic heterogeneity. Clinical reports, based mostly on small samples of patients, may not reflect the true spectrum of pathology of this condition. We have studied the entire range of morpho...
متن کاملAn unusual case of congenitally unguarded tricuspid valve orifice associated with pulmonary valve atresia and intact ventricular septum.
We report on a premature neonate who presented with cyanosis soon after birth. She was found on echocardiography to have an unguarded tricuspid valve orifice associated with pulmonary valve atresia and an intact interventricular septum. Owing to the small-sized pulmonary arteries, she was initially managed conservatively with prostaglandin infusion, and at one year of age underwent a successful...
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ژورنال
عنوان ژورنال: The Journal of Thoracic and Cardiovascular Surgery
سال: 1993
ISSN: 0022-5223
DOI: 10.1016/s0022-5223(19)34123-6